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HERDIN Record #: 100731-19121008051219 Submitted: 10 December 2019 Modified: 10 December 2019

Total anomalous pulmonary venous return in pediatrics: a case series.

Sheryll Dell  C. Reyes

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Total anomalous pulmonary venous connection (TAPVC) is a very uncommon cyanotic anomaly comprising1% of all congenital heart diseases. Since pulmonary veins drain into the systemic venous circulation, TAPVC is incompatible with life unless a communication between the right and left sides of the heart exists; usually via a patent foramen ovale or atrial septal defect. As the right to left shunt is usually small, right heart dilatation and failure ensues owing to a volume overload. Stenosis and obstruction of varying degree at the junction of the anomalous trunk with the vena cava leads to severe pulmonary hypertension which further worsens right heart failure. Patients presenting early infancy with bluish discoloration exaggerated by activity and symptoms of heart failure .They are usually severely acidotic and cyanotic. Without surgery most infants die by 12months of age. However, post-operative mortality is also high owing to increased pulmonary vascular resistance and inadequate repair due to obscure anatomy, the purpose of this case report is to highlight the fact that best postoperative care is the key element of thankful outcome.Even with best of care misdiagnosis can happen. The main objective of this paper is to present 3 cases of patients who presented with a complaint of cyanosis and difficulty of breathing on admission.

Publication Type
Research Project
Date
January 1, 2014
LocationLocation CodeAvailable FormatAvailability
Philippine Heart Center Medical Library CR.010.14 Fulltext Print Format